Abstract. ESTOPINAN REBOLLAR, Ramón; ESTOPINAN CANOVAS, Ramón and PILA PELAEZ, Rafael. Enfermedad de Hirschsprung en un adulto. Rev Col. Resumen. LOMBANA, Luis Jorge y DOMINGUEZ, Luis Carlos. Surgery in adult Hirschsprung’s disease. Rev Col Gastroenterol [online]. , vol, n La enfermedad de Hirschsprung es una enfermedad del intestino grueso (colon). Normalmente, las heces fecales son empujadas a través del colon por.

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Diagnosis requires imaging and rectal manometry and confirmation by histopathology. Show more Show less. It is a rare condition that affects 1: Enfermedad de Hirschsprung en un adulto. It can cause symptoms of severe chronic constipation or frequent episodes of fecal impaction.

Only a small number of cases remain undiagnosed after 5 years of age 2. In our case, we are in a situation of irreversible dilatation of entire colon, so we opted for a total colectomy, restoring intestinal transit by ileo-rectal anastomosis.

IHC x positive for S in the nerve plexuses. Subscribe to our Newsletter. After that, the palpable mass disappeared, but clinical constipation persisted. We report a case not previously diagnosed, which presented hirschsptung a massive colonic dilatation with a maximum diameter of 44 cm, with imminent risk of drilling that forced to perform an emergency surgery.

J Forensic Sci ; There was neuronal dysplasia with scarce presence of ganglion cells on both edges of resection.


Vólvulo en adultos

Hirschsprung’s disease in adults: Treatment is always surgical. In addition, the reported symptoms caused the girl’s parents to begin to justify such a fact as a result of some psychological, rather than organic, disorder.

Given the low incidence of HD in adults, it is difficult to compare different procedures. Several procedures have been designed to treat HD, of which the most important are the following 7: It consists in a rear section of muscular wall of rectum starting adultks dentate line by transanal waywhich removes some of the top segment of internal anal sphincter, getting relief stenosis.

The treatment of choice is surgical and aganglionic segment resection and anastomosis of the healthy colonic segment to the anal canal can be performed laparoscopically. South Med J ; We can conclude that HD is a rare entity in adults and should be suspected in patients with megacolon with a hirschsprunb of constipation refractory to treatment since childhood. Introduction Hirschsprung’s disease HD is a malformation of the large intestine characterized by the absence of ganglion cells in submucosal and myenteric plexus, which produces a functional obstruction and dilatation proximal to the affected segment 1.

The scientific works include the areas of Clinical, Endoscopic, Surgical, and Pediatric Gastroenterology, along with related disciplines.

Diagnóstico tardio da doenc¸a de Hirschsprung

horschsprung Niger J Clin Pract. When he arrived at the hospital, he told doctors that he had not had a bowel movement for 83 days. The pathologist’s report showed the existence of ulceration foci with acute inflammation in the submucosa.


Conventional anorectal manometry trace showing the absence of the inhibitory rectoanal reflex with the maximum tolerable rectal enffermedad. Some patients reach adulthood without a diagnosis for this disease.

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Enfermedad de Hirschprung del adulto

Discussion HD is a congenital anomaly that occurs due to a discontinuation of the cranial-caudal migration of neural crest cells, which are responsible for innervation of the colon, or when the ganglion cells undergo premature death between 5th and 12th weeks of pregnancy. Si continua navegando, consideramos que acepta su uso. However, post-operative bowel functioning is not always satisfactory. How to cite this article. It should be emphasized that the aganglionic segment is strictured.

Surgery was recommended, but his family did not give their permission.